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中文名称：IVD 抗原（重组蛋白）
英文名称： IVD Antigen (Recombinant Protein)
别 名： isovaleryl-CoA dehydrogenase; ACAD2
储 存： 冷冻（-20℃）
相关类别： 抗原
概述
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Fusion protein corresponding to a region derived from 224-423 amino acids of human IVD |
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Full name: |
isovaleryl-CoA dehydrogenase |
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Synonyms: |
ACAD2 |
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Swissprot: |
P26440 |
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Gene Accession: |
BC017202 |
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Purity: |
>85%, as determined by Coomassie blue stained SDS-PAGE |
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Expression system: |
Escherichia coli |
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Tags: |
His tag C-Terminus, GST tag N-Terminus |
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Background: |
Isovaleryl-CoA dehydrogenase (IVD) is a mitochondrial matrix enzyme that catalyzes the third step in leucine catabolism. The genetic deficiency of IVD results in an accumulation of isovaleric acid, which is toxic to the central nervous system and leads to isovaleric acidemia. Alternatively spliced transcript variants encoding different isoforms have been found for this gene. |
